Abstract

Enfermedad de Castleman unicéntrica paraadrenal

La enfermedad de Castleman (CD) puede definirse como unahiperplasia ganglionar reactiva distintiva. Se reconocen dosentidades dentro de la enfermedad, desde el punto de vistaclínico. Una es la forma unicéntrica o localizada (UCD), quesuele manifestarse como el hallazgo de una masa solitaria coninfrecuentes manifestaciones sistémicas; y la otra es la formamulticéntrica que se presenta con síntomas sistémicos, compromisomultifocal y se asocia a otras enfermedades.

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Author(s): María Virginia Bürgesser, Diego Camps, Patricia Calafat, Ana Diller

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